| H01705 | |
| H number | H01705 |
| Name | Bilateral sudden sensorineural hearing loss |
| Description | Bilateral sudden sensorineural hearing loss (SNHL) represents a rare disease entity, constituting less than 5 % of all sudden SNHL cases. Unlike unilateral disease, bilateral sudden SNHL appears to be mostly related to serious systemic pathology, and is associated with a more severe degree of hearing loss, poorer prognosis following treatment, and more significant impairment in morbidity and overall quality of life. |
| Category | Nervous system disease |
| Network | - |
| Gene | ACTG1 [HSA:71] [KO:K05692] CDH23 [HSA:64072] [KO:K06813] COCH [HSA:1690] [KO:K23574] KCNQ4 [HSA:9132] [KO:K04929] TECTA [HSA:7007] [KO:K18273] TMPRSS3 [HSA:64699] [KO:K09634] WFS1 [HSA:7466] [KO:K14020] |
| Pathogen | - |
| Env factor | - |
| Carcinogen | - |
| Drug | - |
| Comment | See also H01704 Sudden sensorineural hearing loss, H00604 Deafness, autosomal dominant, and H00605 Deafness, autosomal recessive. |
| Other DBs | ICD-11: AB51.1 ICD-10: H90.3 H91.2 MeSH: D006312 OMIM: 604717 601386 601369 600101 601543 603629 601072 600965 |
| Reference | PMID:24331736 AUTHORS Sara SA, Teh BM, Friedland P TITLE Bilateral sudden sensorineural hearing loss: review. JOURNAL J Laryngol Otol 128 Suppl 1:S8-15 (2014) DOI:10.1017/S002221511300306X PMID:26944135 AUTHORS Chen YH, Young YH TITLE Bilateral simultaneous sudden sensorineural hearing loss. JOURNAL J Neurol Sci 362:139-43 (2016) DOI:10.1016/j.jns.2016.01.029 PMID:20301607 AUTHORS Smith RJH, Shearer AE, Hildebrand MS, Van Camp G TITLE Deafness and Hereditary Hearing Loss Overview JOURNAL GeneReviews (1993) |