| H01687 | |
| H番号 | H01687 |
| 名称 | 肝外門脈閉塞症 |
| 概要 | Extrahepatic portal vein obstruction (EHPVO) is a vascular disorder of liver characterized by obstruction and cavernomatous transformation of portal vein with or without the involvement of intrahepatic portal vein, splenic vein, or superior mesenteric vein. The most characteristic imaging manifestation is the formation of porto-portal collaterals that allow hepatopetal flow. Gradually there is organization and temporal evolution of thrombus with formation of portal collaterals termed "cavernoma" aiming to bypass the obstructed portal vein. Patients generally present in childhood with multiple episodes of variceal bleed and EHPVO is the predominant cause of paediatric portal hypertension (PHT) in developing countries. |
| カテゴリ | 消化器系疾患 |
| ネットワーク | - |
| 病因遺伝子 | - |
| 病原体 | - |
| 環境要因 | - |
| 発癌物質 | - |
| 治療薬 | - |
| コメント | See also H01686 Idiopathic portal hypertension |
| リンク | ICD-11: DB98.3 ICD-10: I81 |
| 文献 | PMID:27358683 著者 Pargewar SS, Desai SN, Rajesh S, Singh VP, Arora A, Mukund A タイトル Imaging and radiological interventions in extra-hepatic portal vein obstruction. 雑誌 World J Radiol 8:556-70 (2016) DOI:10.4329/wjr.v8.i6.556 PMID:26111208 著者 Arora A, Sarin SK タイトル Multimodality imaging of primary extrahepatic portal vein obstruction (EHPVO): what every radiologist should know. 雑誌 Br J Radiol 88:20150008 (2015) DOI:10.1259/bjr.20150008 PMID:26021771 著者 Wani ZA, Bhat RA, Bhadoria AS, Maiwall R タイトル Extrahepatic portal vein obstruction and portal vein thrombosis in special situations: Need for a new classification. 雑誌 Saudi J Gastroenterol 21:129-38 (2015) DOI:10.4103/1319-3767.157550 |