| H01858 | |
| H番号 | H01858 |
| 名称 | 総排泄腔遺残 |
| 概要 | Persistent cloaca is an uncommon congenital anomaly in which there is a single perineal opening for the urinary, gastrointestinal, and reproductive tracts. It is the most severe form of anorectal malformation encountered in girls. The incidence is approximately 1 in 50,000 live births. Persistent cloaca results from abnormal development of the cloacal membrane before 50 days post fertilization. In addition to a single perineal opening, secondary urogenital or gastrointestinal anomalies are often associated with persistent cloaca. Moreover, anomalies of other organ systems such as cardiac or skeletal malformations are known to coexist. The common channel of persistent cloaca varies from 1 cm to 10 cm. Those cases with a common channel longer than 3 cm are predicted with the higher incidence of complications. For patients with a common channel greater than 3 cm, a laparotomy is usually required. |
| カテゴリ | 先天奇形 |
| ネットワーク | - |
| 病因遺伝子 | - |
| 病原体 | - |
| 環境要因 | - |
| 発癌物質 | - |
| 治療薬 | - |
| コメント | - |
| リンク | ICD-11: LB17.2 ICD-10: Q43.7 |
| 文献 | PMID:25981991 著者 Wang C, Li L, Cheng W, Liu S, Diao M, Li X, Qiao G, Zhang Z, Chen Z タイトル A new approach for persistent cloaca: Laparoscopically assisted anorectoplasty and modified repair of urogenital sinus. 雑誌 J Pediatr Surg 50:1236-40 (2015) DOI:10.1016/j.jpedsurg.2015.04.016 PMID:22368130 著者 Livingston JC, Elicevik M, Breech L, Crombleholme TM, Pena A, Levitt MA タイトル Persistent cloaca: a 10-year review of prenatal diagnosis. 雑誌 J Ultrasound Med 31:403-7 (2012) DOI:10.7863/jum.2012.31.3.403 |