| H01007 | |
| H number | H01007 |
| Name | Choroid plexus papilloma |
| Description | Choroid plexus tumors (CPTs) are rare intraventricular papillary neoplasms of neuroectodermal origin, accounting for less than 1% of all intracranial tumors and 2-4% of pediatric brain tumors. CPTs are categorized by three distinct histologies; choroid plexus papilloma, atypical choroid plexus papilloma, and the malignant choroid plexus carcinoma. Choroid plexus papillomas outnumber choroid plexus carcinomas and are composed of a single layer of cuboidal-to-columnar cells, resting on a basement membrane overlying papillary and vascularized connective tissue. |
| Category | Nervous system disease |
| Network | - |
| Gene | p53 [HSA:7157] [KO:K04451] |
| Pathogen | - |
| Env factor | - |
| Carcinogen | - |
| Drug | - |
| Comment | - |
| Other DBs | ICD-11: 2A00.22 ICD-10: D33.0 MeSH: D020288 OMIM: 260500 |
| Reference | PMID:3217283 AUTHORS Tomita T, McLone DG, Flannery AM TITLE Choroid plexus papillomas of neonates, infants and children. JOURNAL Pediatr Neurosci 14:23-30 (1988) DOI:10.1159/000120358 PMID:21990040 AUTHORS Gozali AE, Britt B, Shane L, Gonzalez I, Gilles F, McComb JG, Krieger MD, Lavey RS, Shlien A, Villablanca JG, Erdreich-Epstein A, Dhall G, Jubran R, Tabori U, Malkin D, Finlay JL TITLE Choroid plexus tumors; management, outcome, and association with the Li-Fraumeni syndrome: the Children's Hospital Los Angeles (CHLA) experience, 1991-2010. JOURNAL Pediatr Blood Cancer 58:905-9 (2012) DOI:10.1002/pbc.23349 PMID:21970783 AUTHORS Ogiwara H, Dipatri AJ, Alden TD, Bowman RM, Tomita T TITLE Choroid plexus tumors in pediatric patients. JOURNAL Br J Neurosurg 26:32-7 (2012) DOI:10.3109/02688697.2011.601820 PMID:11135453 AUTHORS Rickert CH, Paulus W TITLE Tumors of the choroid plexus. JOURNAL Microsc Res Tech 52:104-11 (2001) DOI:10.1002/1097-0029(20010101)52:1<104::AID-JEMT12>3.0.CO;2-3 PMID:22059144 AUTHORS Imai M, Tominaga J, Matsumae M TITLE Choroid plexus papilloma originating from the cerebrum parenchyma. JOURNAL Surg Neurol Int 2:151 (2011) DOI:10.4103/2152-7806.86228 |