| H01687 | |
| H number | H01687 |
| Name | Extrahepatic portal vein obstruction; Extrahepatic portal venous obstruction |
| Description | Extrahepatic portal vein obstruction (EHPVO) is a vascular disorder of liver characterized by obstruction and cavernomatous transformation of portal vein with or without the involvement of intrahepatic portal vein, splenic vein, or superior mesenteric vein. The most characteristic imaging manifestation is the formation of porto-portal collaterals that allow hepatopetal flow. Gradually there is organization and temporal evolution of thrombus with formation of portal collaterals termed "cavernoma" aiming to bypass the obstructed portal vein. Patients generally present in childhood with multiple episodes of variceal bleed and EHPVO is the predominant cause of paediatric portal hypertension (PHT) in developing countries. |
| Category | Digestive system disease |
| Network | - |
| Gene | - |
| Pathogen | - |
| Env factor | - |
| Carcinogen | - |
| Drug | - |
| Comment | See also H01686 Idiopathic portal hypertension |
| Other DBs | ICD-11: DB98.3 ICD-10: I81 |
| Reference | PMID:27358683 AUTHORS Pargewar SS, Desai SN, Rajesh S, Singh VP, Arora A, Mukund A TITLE Imaging and radiological interventions in extra-hepatic portal vein obstruction. JOURNAL World J Radiol 8:556-70 (2016) DOI:10.4329/wjr.v8.i6.556 PMID:26111208 AUTHORS Arora A, Sarin SK TITLE Multimodality imaging of primary extrahepatic portal vein obstruction (EHPVO): what every radiologist should know. JOURNAL Br J Radiol 88:20150008 (2015) DOI:10.1259/bjr.20150008 PMID:26021771 AUTHORS Wani ZA, Bhat RA, Bhadoria AS, Maiwall R TITLE Extrahepatic portal vein obstruction and portal vein thrombosis in special situations: Need for a new classification. JOURNAL Saudi J Gastroenterol 21:129-38 (2015) DOI:10.4103/1319-3767.157550 |