H00691
H number H00691
Name Bullous congenital ichthyosiform erythroderma (BCIE);
Epidermolytic hyperkeratosis (EHK)
Description Bullous congenital ichthyosiform erythroderma (BCIE), also known as bullous congenital ichthyosiform erythroderma, is characterized by erythema and skin blistering of the newborn. The erythema is replaced with thick scaling later. Neonates with BCIE have higher risk of developing severe infection, such as sepsis.
Category Skin and connective tissue disease