H00750
H number H00750
Name Keratosis follicularis spinulosa decalvans
Description Keratosis follicularis spinulosa decalvans (KFSD) is a rare genodermatosis characterized by hyperkeratotic follicular papules with progressive alopecia of the scalp and photophobia. It is initially described as a sex-linked disorder with typical palmoplantar keratoderma, but autosomal dominant form with marked erythema has been observed as well.
Category Skin and connective tissue disease